A Gastric Perivascular Epithelioid Cell Tumor: A Case Report

نویسندگان

  • Baptiste Abbar
  • Frédéric Charlotte
  • Jean Michel Coindre
  • Philippe Spano
چکیده

Perivascular epithelioid cell tumors (PEComas) of gastro intestinal tract are very rare, with only few cases reported in the literature. The PEComas are a family of rare mesenchymal tumors characterized by perivascular epithelioid cell differentiation. We herein report our experience with a patient who had a primary gastric PEComa that was diagnosed by an expert pathologist review of the excised tissues and which showed neopastic epithelioid cells arranged as sheets with abundant eosinophilic cytoplasm, nuclei with a prominent nucleolus and expressed melanocytic and muscle markers.

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تاریخ انتشار 2016